{"id":187,"date":"2022-09-07T12:39:00","date_gmt":"2022-09-07T07:09:00","guid":{"rendered":"https:\/\/drpavankumar.in\/blog\/?p=187"},"modified":"2025-06-18T18:26:41","modified_gmt":"2025-06-18T12:56:41","slug":"papvc-sinus-venosus-defect-heart-surgery","status":"publish","type":"post","link":"https:\/\/drpavankumar.in\/blog\/papvc-sinus-venosus-defect-heart-surgery\/","title":{"rendered":"PAPVC + SINUS VENOSUS DEFECT HEART SURGERY."},"content":{"rendered":"\r\n<p>Mr. IK 42 years male complained about breathlessness on exertion since last 2 years . On<br>investigations chest X\u2019ray chest showed moderate enlarged heart &amp; routine Echo cardiogragrapy<br>Showed high pulmonary artery pressure artery pressure &amp; right ventricular overload, but failed to<br>show any congenital hole in the heart. Later transesophegeal Echo showed up sinus venosus type<br>Atrial Septal Defect (ASD). CT scan pulmonary angiography showed that Right superior &amp; middle<br>pulmonary veins draining into right atrium via Supeior vena cava( SVC) making a diagnosis of right<br>partial Anomalous Pulmonary venous Connection ( PAPVC).<br>Cardiac catheterisation on patient showed predominant left to right shunt across sinus venosus ASD<br>with severely high Pulmonary Artery pressure .<br>Patient was taken up for Open Heart Surgery repair on 8 March\u20192019 at BSES hospital by Dr. Pavan<br>Kumar. During his surgery findings showed that he had 4.5 x 4.5 cm2 large sinus venous ASD with<br>patent foramen Ovale ( PFD ). PAPVC drained into SVC. 6cm Large DACRON Patch was then used<br>to Re-route PAPVC drain into left Atrium with closure of Sinus Venosus ASD which included of<br>PFO repair. Surgery went off very well &amp; patient had uneventful recovery.<\/p>\r\n\r\n\r\n\r\n<p>Discussion \u2013 Sinus Venosus ASD are less common variety of Secundum ASD disease less than 5%<br>patient have sinus venosaus ASD of all secundum variety. In about 50% such cases Right PAPVC is<br>found.<br>These are difficult to diagnose by normal Echo . CT scan chest with pulmonary angiogram is usually<br>diagnostic of PAPVC. Surgical correction is only treatment of choice with assured success.<\/p>\r\n","protected":false},"excerpt":{"rendered":"<p>Mr. IK 42 years male complained about breathlessness on exertion since last 2 years . Oninvestigations chest X\u2019ray chest showed moderate enlarged heart &amp; routine Echo cardiogragrapyShowed high pulmonary artery pressure artery pressure &amp; right ventricular overload, but failed toshow any congenital hole in the heart. Later transesophegeal Echo showed up sinus venosus typeAtrial Septal [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":211,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1],"tags":[],"class_list":["post-187","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-angioplasty"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.9 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Best Cardiac Surgeon in Mumbai | Trusted Heart Surgery Expert<\/title>\n<meta name=\"description\" content=\"Mr. IK 42 years male complained about breathlessness on exertion since last 2 years. 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